久久99精品久久久久久无毒不卡,高潮videossex潮喷另类,秀色app视频,chinesefree高潮抽搐

歡迎來到北京博奧森生物技術(shù)有限公司網(wǎng)站！
咨詢熱線

18611424007

當(dāng)前位置：首頁  >  產(chǎn)品中心  >  抗體/抗原  >  一抗  >  bsm-62371Rβ葡萄糖醛酸苷酶重組兔單抗

β葡萄糖醛酸苷酶重組兔單抗

簡要描述：Defects in GUSB are the cause of mucopolysaccharidosis type 7 (MPS7) ; also known as Sly syndrome. MPS7 is an autosomal recessive lysosomal storage disease characterized by inability to degrade glucuronic acid-containing glycosaminoglycans. The phenotype is highly variable, ranging from severe lethal hydrops fetalis to mild forms with survival into adulthood. Most patients with the intermediate phenotype show hepatomegaly, skeletal anomalies, coarse facies, and variable degrees of mental impai

  • 產(chǎn)品型號：bsm-62371R
  • 廠商性質(zhì)：生產(chǎn)廠家
  • 更新時間：2025-03-03
  • 訪  問  量： 148

詳細介紹

Human
WB,IHC-P,IHC-F,ICC/IF,IF,Flow-Cyt
Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles.

產(chǎn)品咨詢

留言框

  • 產(chǎn)品：

  • 您的單位：

  • 您的姓名：

  • 聯(lián)系電話：

  • 常用郵箱：

  • 省份：

  • 詳細地址：

  • 補充說明：

  • 驗證碼：

    請輸入計算結(jié)果（填寫阿拉伯?dāng)?shù)字），如：三加四=7